Fig. 2

Metabolic map of fumarate hydratase deficiency
Abbreviations: ADSL Adenylosuccinate lyase; AICAR Aminoimidazolecarboxamide ribose; SAICAR Succinylaminoimidazolecarboxamide ribose
Metabolic map of fumarate hydratase deficiency
Abbreviations: ADSL Adenylosuccinate lyase; AICAR Aminoimidazolecarboxamide ribose; SAICAR Succinylaminoimidazolecarboxamide ribose